Paratesticular region is a rare localization for tumor development. However, a great variety of tumors is observed due to its complicated embryological origin and various anatomical structures in the area. Clinical and radiological findings are important for diagnosis and guidance of surgical treatment. While ultrasonography is the primary diagnostic tool, computed tomography and magnetic resonance imaging are helpful on benign-malignant differentiation and staging of malignant tumors. Adenomatoid tumor, lipoma and leiomyoma are most frequently confronted benign neoplasms. Sarcomas constitute majority of malignant tumors. As rhabdomyosarcoma is frequent in children; liposarcoma, leiomyosarcoma, rhabdomyosarcoma and undifferentiated sarcoma are observed in adults. Tunica vaginalis, that shows continuity with peritoneum, is the source for mesothelioma. Ovarian type epithelial tumors originate from Müllerian remnants and metaplasia of mesothelium. Excision is curative for benign tumors. Radical inguinal orchiectomy with high cord ligation is preferred in case of malignancy. However, the role of lymphadenectomy, radiotherapy and chemotherapy is controversial due to limited number of cases. A multidisciplinary team is essential that consists of urooncologist, radiologist, pathologist and oncologist for best approach as paratesticular tumors are similar in the way of clinical, histological and radiological features.

Keywords: Paratestis, tumor, diagnosis, pathology