ABSTRACT

Histopathological classification of renal tumours is forming a long list of entities with additionally described new subtypes. In 2004 WHO classification renal tumours are separated mainly renal cell, metanephric, nephroblastic, mixt mesenchimal and epithelial, mesenchimal, neuroendocrine tumors. Neuroblastoma and pheochromocytoma have formed two other different categories. In daily practice most of the tumors are renal cell carcinomas, mostly consisting of clear cell, papillary and chromophobe subtypes. The other rare tumours would lead potential problems in differential diagnosis for pathologists, and when evaluating the clinical approach of urologist. The aim of this article is to review recent literature on rare renal tumours within histopathological, clinical and molecular aspects.